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There is extensive varicose and cystic bronchiectasis, severely affecting the left lower lobe. Consolidation/atelectatic changes are seen involving the left lower lobe. There are areas of tree-in-bud appearance. There is no evidence of pleural effusion or pneumothorax. Consistent with diffuse lung disease of cystic fibrosis.

The remainder of her transplant assessment included normal baseline labs, except for a capillary blood gas demonstrating a slightly elevated pCO2 of 51 mmHg. Ventilation-perfusion scan demonstrated 24% of the ventilation and perfusion to the left lung. Her six minute walk showed significant impairment, but more notably, a saturation of 84 – 86% pre-walk, and 74% post. ECG and echocardiogram were normal.

Sputum culture was sent for microbiology, and showed ongoing growth of Pseudomonas aeruginosa, Burkholderia cepacia complex (genomovar V), Staphylococcus aureus, Stenotrophomonas maltophilia, and Aspergillus.

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