Clara Fernandez Elviro, MD
BC Children’s Hospital, Vancouver, BC

The case of a 10-year-old girl with cystic fibrosis and persistent atelectasis secondary to inflammatory tissue will be presented. Since 2018, chest X-ray showed persistent consolidation and atelectasis in the right upper lobe associated with recurrent chest exacerbations every 4-6 weeks. Several bronchoscopies for diagnostic and unsuccessful therapeutic purposes were done. However, and despite antibiotic prophylaxis, each attempt resulted in the recurrence of an inflammatory polyp leading to the obstruction of the airway and subsequently the recurrence of chest infections. More aggressive treatment options such as lobectomy have been discussed. However, there is hope that a trial with a new-generation modulator could be a less invasive alternative. The central role of bronchoscopy in the diagnosis and treatment of persistent atelectasis is illustrated in this case. Moreover, the challenges and uncertainty that surround the treatment of persistent atelectasis in cystic fibrosis patients will be discussed.

Learning Objectives
At the end of this presentation, attendees will be able to:

  • Recognize the utility of bronchoscopy in the management of atelectasis; and
  • Review different strategies used to treat endoluminal lesions.

CanMEDS Roles Addressed: Collaborator, Scholar